Adolescence with Duchenne and Becker muscular dystrophy: a cardiac magnetic resonance comparison study


Duchenne muscular dystrophy (DMD) is the most common neuromuscular disease with high prevalence of DMD-associated heart disease as defined by late gadolinium enhancement (LGE) indicative of myocardial fibrosis and ventricular dysfunction by ejection fraction (EF) that is progressive. The use of cardiac magnetic resonance imaging (CMR) is standard at our institution for DMD patients when sedation is no longer required. LGE by CMR occurs early in DMD patients and is an established marker of myocardial fibrosis preceding systolic dysfunction.


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