Myotonic dystrophy type 1 (DM1) is a multisystemic neuromuscular disease and cardiac involvement occurs in 80% of DM1 and it is the most common cause of sudden death. Few studies have illustrated cardiac involvements constituting of left ventricular tachycardia, ventricular fibrillation, conduction defects and arrhythmia. The aim of our study was to find an additional echocardiographic abnormality in the early stage of DM1 that correlate with the CTG repeat length. 21 genetically confirmed ambulatory DM1 patients were enrolled in this retrospective study.

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